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DeCS
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Descriptor English:
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Hirschsprung Disease
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Descriptor Spanish:
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Enfermedad de Hirschsprung
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Descriptor Portuguese:
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Doença de Hirschsprung
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Synonyms English:
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Aganglionic Megacolon
Aganglionosis, Rectosigmoid Colon
Aganglionosis, Total Colonic
Congenital Intestinal Aganglionosis
Congenital Megacolon
Hirschsprung's Disease
Megacolon, Aganglionic
Rectosigmoid Aganglionosis
Total Colonic Aganglionosis
Aganglionosis, Rectosigmoid
Disease, Hirschsprung
Disease, Hirschsprung's
Hirschsprungs Disease
Rectosigmoid Colon Aganglionosis
Megacolon, Congenital
Aganglionosis, Colonic
Colonic Aganglionosis
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Tree Number:
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C06.198.439
C06.405.469.158.701.439
C16.131.314.439
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Definition English:
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Congenital MEGACOLON resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the LARGE INTESTINE. The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the RECTUM and SIGMOID COLON. |
Indexing Annotation English:
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acquired megacolon = MEGACOLON
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History Note English:
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83; was HIRSCHSPRUNG'S DISEASE see MEGACOLON 1963-82
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Allowable Qualifiers English:
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Record Number:
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6786
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Unique Identifier:
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D006627
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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